6型胶原重组兔单抗

bsm-61026R

重组兔单抗、mIHC精品抗体

Collagen VI Recombinant Rabbit mAb

6型胶原重组兔单抗

BTHLM1; BTHLM1A; OPLL; UCHMD1; UCHMD1A; BTHLM1B; PP3610; UCMD1; UCMD1B; BTHLM1C; DYT27; UCMD1C; Col6a-1; Col6a-2; Col6a-3; RGD1565398; CO6A1_HUMAN; COL6A1; CO6A2_HUMAN; COL6A2; CO6A3_HUMAN; COL6A3; CO6A2_MOUSE; CO6A1_MOUSE;

Rabbit

A synthesized peptide derived from human Collagen VI: 15-250

IgG

Liquid

affinity purified by Protein A

Recombinant

4D10

106

0.01M TBS(pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.

Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.

This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.

The collagens are a superfamily of proteins that play a role in maintaining the integrity of various tissues. Collagens are extracellular matrix proteins and have a triple-helical domain as their common structural element. Collagen VI is a major structural component of microfibrils. The basic structural unit of collagen VI is a heterotrimer of the alpha1(VI), alpha2(VI), and alpha3(VI) chains. The alpha2(VI) and alpha3(VI) chains are encoded by the COL6A2 and COL6A3 genes, respectively. The protein encoded by this gene is the alpha 1 subunit of type VI collagen (alpha1(VI) chain). Mutations in the genes that code for the collagen VI subunits result in the autosomal dominant disorder, Bethlem myopathy. [provided by RefSeq, Jul 2008]